Home
- Questions About Raises, Shuttle Fees Top Administrators Forum
A UAMS Update article about Meet Your Administrator”
- Gruenwald Is New U.S. Citizen
Michael Gruenwald becomes U.S. citizen
- Gruenwald Is New U.S. Citizen
Michael Gruenwald becomes U.S. citizen
- Doughnut Sale to Help UAMS Psychiatry Youth Program
A UAMS Update article about a bake sale
- Call-in Announcements, Forums Will Give Employees More Information
A UAMS Update article about plans to improve communication between administration and employees of UAMS Medical Center
- IT Help Desk 400,000th Call Sweepstakes
IT Help Desk 400,000th Call Sweepstates
- The UAMS Help Desk Today - Ten Years Later
The UAMS Help Desk Today - Ten Years Later
- Free Tickets for UAMS Nights at Ray Winder Field
A UAMS Update article about UAMS Night with the Travelers
- ARIA Training Sessions May 19 - June 27 at UAMS
A UAMS Update article about May 19 - June 27 training sessions
- Human Research Forum Is May 21
A UAMS Update article about human research Q & A
- Accolades, May 2003
Accolades to UAMS faculty and staff
- GCRC Deadline Changed to July 1 for Grant Proposals
A UAMS Update article about GCRC pilot grants
- History of the Help Desk
- Watch, Look & Listen: Preview of New UAMS Public Service Campaign
- Forum to Discuss Impact of HIPAA on Research
Update article about HIPAA and research at UAMS
- Human Research Q and A Forum June 27
A UAMS Update article about the human research forum
- Emailed Version of UAMS Notice of Privacy Practices
UAMS Notice of Privacy Practices
- Free UAF Symposium Aug. 14-15 on Evolution of Human Diet
A UAMS Update article about a diet symposium at UAF
- Tom Butler is Arkansas Administrator of the Year
Tom Butler of UAMS Is Arkansas Administrator of the Year
- Join the Prostate Cancer Race Walk. Click Here for Registration Form.*
Join the Prostate Cancer Race Walk. Click Here for Registration Form.
- Join the Prostate Cancer Race Walk. Click Here for Registration Form.*
Join the Prostate Cancer Race Walk. Click Here for Registration Form.
- Defense Department Funds Possible Therapeutic Vaccine for Ovarian Cancer at UAMS
Defense Department Funds Possible Therapeutic Vaccine for Ovarian Cancer at UAMS
- Defense Department Funds Possible Therapeutic Vaccine for Ovarian Cancer at UAMS
Defense Department Funds Possible Therapeutic Vaccine for Ovarian Cancer at UAMS
- Join UAMS/ACRC Team in Race for the Cure®!
Join UAMS/ACRC Team in Race for the Cure!
- Join UAMS/ACRC Team in Race for the Cure®!
Join UAMS/ACRC Team in Race for the Cure!
- UAMS Scientist Receives $272,000 Grant for Tailoring Cancer Treatments with Laser Test
UAMS Scientist Receives $272,000 Grant for Tailoring Cancer Treatments with Laser Test
- UAMS Scientist Receives $272,000 Grant for Tailoring Cancer Treatments with Laser Test
UAMS Scientist Receives $272,000 Grant for Tailoring Cancer Treatments with Laser Test
- Photo Album: Stephens Institute Was a Highlight of Medicine Alumni Reunion
Photo Album: Stephens Institute Was a Highlight of Medicine Alumni Reunion
- Kids First in Fort Smith Celebrated Fourth in Style
Kids First in Fort Smith Celebrated Fourth in Style
- Class of 1948 Dedicates Endowment to Excellence in Education
Class of 1948 Dedicates Endowment to Excellence in Education
- Pharmacy Professor Elected to American College of Clinical Pharmacy
Pharmacy Professor Elected to American College of Clinical Pharmacy
- Pharmaceutical Scientists, Graduate Students Meet at UAMS
Pharmaceutical Scientists, Graduate Students Meet at UAMS
- Stephanie Gardner, Pharm.D., Ed.D., Is Interim Dean of College of Pharmacy
Stephanie Gardner, Pharm.D., Ed.D., Is Interim Dean of College of Pharmacy
- New COPH Survey Research Expert Eager to Develop New Ways of Measuring Public Health
New COPH Survey Research Expert Eager to Develop New Ways of Measuring Public Health
- Ready, Set, Go! UAMS, KATV Launch Get Healthy Arkansas™
UAMS, KATV Launch Get Healthy Arkansas™
- Osteoarthritis
Osteoarthritis
- Osteoporosis
Osteoporosis
- Panic Disorder
Panic Disorder
- Parkinson's Disease
Parkinson's Disease
- Phobias
Phobias
- Polycystic Ovary Syndrome
Polycystic ovary syndrome
- Rectal Bleeding
Rectal Bleeding
- Renal Failure
Renal Failure
- Schizophrenia
Schizophrenia
- Seizure
Seizure
- Sexually Transmitted Disease
Sexually transmitted disease
- Shortness of Breath
Shortness of Breath
- Shoulder Injuries
Shoulder Injuries
- Sinusitis
Sinusitis
- Skin cancer
Skin cancer
- Sleep Disorders
Sleep Disorders
- Spina bifida
Spina bifida
- Sports Injuries
Sports injuries
- Stress Test
Stress test
- Stroke
Stroke
- Transplantation
transplantation
- Trauma
Trauma
- Trigeminal Neuralgia
Trigeminal Neuralgia
- Warts
Warts
- High Blood Pressure
High Blood Pressure
- Bone Cancer
Bone Cancer
- Cervical Cancer
Cervical Cancer
- Chest Pain
Chest Pain
- Thoracic Surgery
Thoracic Surgery
- Congestive Cardiomyopathy
Congestive Cardiomyopathy
- Hypertrophic Cardiomyopathy
Hypertrophic Cardiomyopathy
- Restrictive Cardiomyopathy
Restrictive Cardiomyopathy
- Cholesteatoma
Cholesteatoma
- Intermittent Claudication
Intermittent Claudication
- Congenital Heart Disease
Congenital Heart Disease
- Fibroid
Fibroid
- Bone Densitometry
Bone Densitometry
- Breast MRI
Breast MRI
- Ear Surgery
Ear Surgery
- Death
Death
- Foot Problems
Foot Problems
- Fungal Infections
Fungal Infections
- Gynecologic Cancer
Gynecologic Cancer
- Gynecology
Gynecology
- Hand Problems
Hand Problems
- Kidney Disease
kidney disease
- Labatory Diagnosis
Labatory Diagnosis
- Liver Disease
Liver Disease
- Macular Degeneration
Macular Degeneration
- Kidney Transplantation
Kidney Transplantation
- Recurrent Miscarriage
Recurrent Miscarriage
- Pedriatric Surgery
Pedriatric Surgery
- Sex Abuse
Sex Abuse
- Dysphagia
Dysphagia
- Trauma
Trauma
- Uterine Cancer
Uterine Cancer
- Foot Ulcer
Foot Ulcer
- Pregnancy Complications
Pregnancy Complications
- Travel Medicine
Travel Medicine
- Shortness of Breath
Shortness of Breath
- Prostate Problems
Prostate Problems
- Primary Care
Primary Care
- Vocal Cord Paralysis
Vocal Cord Paralysis
- Hoarseness
Hoarseness
- Weight Control
Weight Control
- Balance Problems
Balance Problems
- Back Pain
Back Pain
- Brain Injury
Brain Injury
- Heart Diseases
Heart Diseases
- Autonomic Nervous System Disorders
Autonomic Nervous System Disorders
- Jason's Deli to Donate 10 Percent of Sales to the College of Nursing Student Nurses
Jason's Deli to Donate 10 Percent of Sales to the College of Nursing Student Nurses
- Cancer Institute Gift Shop to Hold 20 Percent Off Sale
Cancer Institute Gift Shop to Hold 20 Percent Off Sale
- Cancer Institute Gift Shop to Hold 20 Percent Off Sale
Cancer Institute Gift Shop to Hold 20 Percent Off Sale
- SAP and ESS Portal Upgrade
SAP and ESS Portal Upgrade
- Overcoming Adversity All Worth It, Says UAMS Researcher
Nov. 9, 2009 | A summer research internship hooked Lee Ann MacMillan-Crow, Ph.D., on science. Even almost failing a neuroscience course her first semester of graduate school did not deter her.
- College of Nursing Faculty, Students Host Bake Sale
College of Nursing Faculty, Students Host Bake Sale
- College of Nursing Faculty, Students Host Bake Sale
College of Nursing Faculty, Students Host Bake Sale
- Additional Employee and Student Parking -- No Waiting List
Additional Employee and Student Parking -- No Waiting List
- Additional Employee and Student Parking -- No Waiting List
Additional Employee and Student Parking -- No Waiting List
- Collier Drug Stores donates $50,000 to UAMS-Northwest
Nov. 12, 2009 | A fourth-generation family drug store chain with roots in Fayetteville has donated $50,000 to the University of Arkansas for Medical Sciences (UAMS) – Northwest.
- UAMS Allied Health College Dean Receives ‘Legacy of Excellence’ Award
LITTLE ROCK – The Association of Schools of Allied Health Professions recently recognized Ronald Winters, Ph.D., dean of the University of Arkansas for Medical Sciences (UAMS) College of Health Related Professions, for his contributions to the field throughout his career.
- Have Your Baby at UAMS and Save up to $1,000
Have Your Baby at UAMS and Save up to $1,000
- Have Your Baby at UAMS and Save up to $1,000
Have Your Baby at UAMS and Save up to $1,000
- Documentum (ApplicationXtender Desktop and Application Web Access) Upgrade
Documentum (ApplicationXtender Desktop and Application Web Access) Upgrade
- Visiting Professor to Give Lecture on Complex Regional Pain Syndrome on Nov. 19
Visiting Professor to Give Lecture on Complex Regional Pain Syndrome on Nov. 19
- Visiting Professor to Give Lecture on Complex Regional Pain Syndrome on Nov. 19
Visiting Professor to Give Lecture on Complex Regional Pain Syndrome on Nov. 19
- November 24, Science Café – ‘Obesity: Young & Old’
November 24, Science Café – ‘Obesity: Young & Old’
- November 24, Science Café – ‘Obesity: Young & Old’
November 24, Science Café – ‘Obesity: Young & Old’
- Sunrise Downtime
Sunrise Downtime
- UAMS Grad Becomes First Clinical Pharmacy Resident at WRMC
Erin Beth Davis Hays returned to Batesville and White River Medical Center to become the first clinical pharmacy resident at the hospital. The residency program, only the fifth in Arkansas, is a joint effort between WRMC, the University of Arkansas for Medical Sciences College of Pharmacy and the North Central Arkansas Area Health Education Center.
- Annual Tree Lights Program Benefits UAMS Auxiliary
Annual Tree Lights Program Benefits UAMS Auxiliary
- Annual Tree Lights Program Benefits UAMS Auxiliary
Annual Tree Lights Program Benefits UAMS Auxiliary
- UAMS Chat System Server Upgrade
UAMS Chat System Server Upgrade
- Honor a Loved One with a Miracle Star at the Cancer Institute this Holiday Season
Honor a Loved One with a Miracle Star at the Cancer Institute this Holiday Season
- Honor a Loved One with a Miracle Star at the Cancer Institute this Holiday Season
Honor a Loved One with a Miracle Star at the Cancer Institute this Holiday Season
- UAMS Bookstore Offers No Waiting for Specialty Coffees and Homemade Fudge
UAMS Bookstore Offers No Waiting for Specialty Coffees and Homemade Fudge
- UAMS Bookstore Offers No Waiting for Specialty Coffees and Homemade Fudge
UAMS Bookstore Offers No Waiting for Specialty Coffees and Homemade Fudge
- Continuing Medical Education Newsletter
Continuing Medical Education Newsletter
- Continuing Medical Education Newsletter
Continuing Medical Education Newsletter
- Logician EMR to Undergo Emergency Maintenance
Logician EMR to Undergo Emergency Maintenance
- Educational Technology Excellence Award Announced
Educational Technology Excellence Award Announced
- Educational Technology Excellence Award Announced
Educational Technology Excellence Award Announced
- Local Church Invites UAMS Employees, Students to Thanksgiving Dinner
Local Church Invites UAMS Employees, Students to Thanksgiving Dinner
- Local Church Invites UAMS Employees, Students to Thanksgiving Dinner
Local Church Invites UAMS Employees, Students to Thanksgiving Dinner
- Campus Wireless Network Downtime
Campus Wireless Network Downtime
|
What is Congenital Heart Defects (Surgery)?
A variety of surgical procedures that are performed to repair the many types of heart defects that may be present at birth.
Heart surgery for congenital defects is performed to repair a defect as much as possible and improve the flow of blood and oxygen to the body. While congenital heart defects vary in their severity, most require surgery. Surgery is recommended for congenital heart defects that result in a lack of oxygen, a poor quality of life, or a patient who does not thrive. Some types of congenital heart defects that don't cause symptoms are treated surgically because they can lead to serious complications.
Table of Contents
Precautions | Description | Preparation | Aftercare | Risks | For More Information | Key Terms
Precautions
There are many types of surgery for congenital heart defects and many considerations in the decision to operate. The patient's cardiologist or surgeon will discuss these issues on an individual basis.
Description
There are many types of congenital heart defects. Most obstruct the flow of blood in the heart, or the vessels near it, or cause an abnormal flow of blood through the heart. Rarer types include newborns born with one ventricle, one side of the heart that is not completely formed, or the pulmonary artery and the aorta coming out of the same ventricle. Most congenital heart defects require surgery during infancy or childhood. Recommended ages for surgery for the most common congenital heart defects are:
- atrial septal defects: during the preschool years
- patent ductus arteriosus: between ages one and two
- coarctation of the aorta: in infancy, if it's symptomatic, at age four otherwise
- tetralogy of Fallot: age varies, depending on the patient's signs and symptoms
- transposition of the great arteries: often in the first weeks after birth, but before the patient is 12 months old
Surgical procedures seek to repair the defect as much as possible and restore circulation to as close to normal as possible. Sometimes, multiple, serial, surgical procedures are necessary. Smaller congenital heart defects can now be repaired in a cardiac catheterization lab instead of an operating room. Catheterization procedures include balloon atrial septostomy and balloon valvuloplasty. Surgical procedures include arterial switch, Damus-Kaye-Stansel procedure, Fontan procedure, Ross procedure, shunt procedure, and venous switch or intra-atrial baffle.
Catheterization procedures
Balloon atrial septostomy and balloon valvuloplasty are cardiac catheterization procedures. Cardiac catheterization procedures can save the lives of critically ill neonates and in some cases eliminate or delay more invasive surgical procedures. It is expected that catheterization procedures will continue to replace more types of surgery for congenital heart defects in the future. A thin tube called a catheter is inserted into an artery or vein in the leg, groin, or arm and threaded into the area of the heart which needs repair. The patient receives a local anesthetic at the insertion site and is awake but sedated during the procedure.
BALLOON ATRIAL SEPTOSTOMY
Balloon atrial septostomy is the standard procedure for correcting transposition of the great arteries; it is sometimes used in patients with mitral, pulmonary, or tricupsid atresia (atresia is a defect that causes the blood to carry too little oxygen to the body). Balloon atrial septostomy enlarges the atrial opening. A special balloon-tipped catheter is inserted into the right atrium and inflated to create a large opening in the atrial septum.
BALLOON VALVULOPLASTY
Balloon valvuloplasty uses a balloon-tipped catheter to open a narrowed heart valve, improving the flow of blood. It is the procedure of choice in pulmonary stenosis and is sometimes used in aortic stenosis. Balloons made of plastic polymers are placed at the end of the catheter and inflated to relieve the obstruction in the heart valve. Long-terms results are excellent in most cases. The operative death rate is 2-4%.
Surgical procedures
These procedures are performed under general anesthesia. Some require the use of a heart-lung machine, which cools the body to reduce the need for oxygen and takes over for the heart and lungs during the procedure.
ARTERIAL SWITCH
Arterial switch is performed to correct transposition of the great arteries, where the position of the pulmonary artery and the aorta are reversed. The procedure involves connecting the aorta to the left ventricle and the pulmonary artery to the right ventricle.
DAMUS-KAYE-STANSEL PROCEDURE
Transposition of the great arteries can also be corrected by the Damus-Kaye-Stansel procedure, in which the pulmonary artery is cut in two and connected to the ascending aorta and right ventricle.
FONTAN PROCEDURE
For tricuspid atresia and pulmonary atresia, the Fontan procedure connects the right atrium to the pulmonary artery directly or with a conduit, and the atrial defect is closed. Survival is over 90%.
PULMONARY ARTERY BANDING
Pulmonary artery banding is narrowing the pulmonary artery with a band to reduce blood flow and pressure in the lungs. It is used for ventricular septal defect, atrioventricular canal defect, and tricuspid atresia. Later, the band can be removed and the defect corrected with open heart surgery.
ROSS PROCEDURE
To correct aortic stenosis, the Ross procedure grafts the pulmonary artery to the aorta.
SHUNT PROCEDURE
For Tetralogy of Fallot, tricuspid atresia, or pulmonary atresia, the shunt procedure creates a passage between blood vessels, sending blood into parts of the body that need it.
VENOUS SWITCH
For transposition of the great arteries, venous switch creates a tunnel inside the atria to re-direct oxygen-rich blood to the right ventricle and aorta and venous blood to the left ventricle and pulmonary artery.
OTHER TYPES OF SURGERY
These surgical procedures are also used to treat common congenital heart defects. A medium to large ventricular or atrial septal defect can be closed by suturing it or covering it with a Dacron patch. For patent ductus arteriosus, surgery consists of dividing the ductus into two and tying off the ends. If performed within the patient's first few years, there is practically no risk associated with this operation. Surgery for coarctation of the aorta involves opening the chest wall, removing the defect, and reconnecting the ends of the aorta. If the defect is too long to be reconnected, a Dacron graft is used to replace the missing piece. In uncomplicated cases, the risk of the operation is 1-2%.
Preparation
Before surgery for congenital heart defects, the patient will receive a complete evaluation, which includes a physical exam, a detailed family history, a chest x ray, an electrocardiogram, an echocardiogram, and usually cardiac catheterization. For six to eight hours before the surgery, the patient cannot eat or drink anything. An electrocardiogram shows the heart's activity and may reveal a lack of oxygen. Electrodes covered with conducting jelly are placed on the patient's chest, arms, and legs and the heart's impulses are traced on paper. An echocardiogram uses sound waves to create an image of the heart's chambers and valves. Gel is applied to a hand-held transducer and then pressed against the patient's chest. Cardiac catheterization is an invasive diagnostic technique used to evaluate the heart in which a long tube is inserted into a blood vessel and guided into the heart. A contrast solution is injected to make the heart visible on x rays.
Aftercare
After heart surgery for congenital defects, the patient goes to an intensive care ward where he or she is connected to a variety of tubes and monitors, including a ventilator. Patients are monitored every 15 minutes until vital signs are stable. Heart sounds, oxygenation, and the electrocardiogram are monitored. Chest tubes will be checked to ensure that they're draining properly and there is no hemorrhage. Pain medications will be administered. Complications such as stroke, lung blood clots, and reduced blood flow to the kidneys will be watched for. After the ventilator and breathing tube are removed, chest physical therapy and exercises to improve circulation will be started.
Risks
Complications from heart surgery for congenital defects can be severe. They include shock, congestive heart failure, lack of oxygen or too much carbon dioxide in the blood, irregular heartbeat, stroke, infection, kidney damage, lung blood clot, low blood pressure, hemorrhage, cardiac arrest, and death.
For More Information
Books
-
"Congenital Heart Disease." In Current Medical Diagnosis and Treatment, 1998. 37th ed. Ed. Stephen McPhee, et al. Stamford: Appleton & Lange, 1997.
-
DeBakey, Michael E., and Antonio M. Gotto Jr. "Congenital Abnormalities of the Heart." In The New Living Heart. Holbrook, MA: Adams Media Corporation, 1997.
-
Park, Myung K. Pediatric Cardiology for Practitioners. 3rd ed. St. Louis: Mosby, 1996.
-
Texas Heart Institute. "Congenital Heart Disease." In Texas Heart Institute Heart Owners Handbook. New York: John Wiley & Sons, 1996.
Periodicals
-
Hicks, George L. "Cardiac Surgery." Journal of the American College of Surgeons 186, no. 2 (Feb. 1998): 129-132.
-
Rao, P. S. "Interventional Pediatric Cardiology: State of the Art and Future Directions." Pediatric Cardiology 19 (1998): 107-124.
Organizations
-
American Heart Association. 7320 Greenville Ave. Dallas, TX 75231. (214) 373-6300. http://www.americanheart.org
-
Children's Health Information Network. 1561 Clark Drive, Yardley, PA 19067. (215) 493-3068. http://www.tchin.org
-
Congenital Heart Anomalies Support, Education & Resources, Inc. 2112 North Wilkins Road, Swanton, OH 43558. (419) 825-5575. http://www.csun.edu/~hfmth006/chaser
-
Texas Heart Institute. Heart Information Service. PO Box 20345, Houston, TX 77225-0345. http://www.tmc.edu/thi
Key Terms
| Term |
Definition |
| Atresia |
A congenital defect in which the blood pumped through the body has too little oxygen. In tricuspid atresia, the baby lacks a triscupid valve. In pulmonary atresia, a pulmonary valve is missing. |
| Coarctation of the aorta |
A congenital defect in which severe narrowing or constriction of the aorta obstructs the flow of blood. |
| Congenital heart defects |
Congenital means conditions which are present at birth. Congenital heart disease includes a variety of defects that babies are born with. |
| Patent ductus arteriosus |
A congenital defect in which the temporary blood vessel connecting the left pulmonary artery to the aorta in the fetus doesn't close in the newborn. |
| Septal defects |
These are holes in the septum, the muscle wall separating the right and left sides of the heart. Atrial septal defects are openings between the two upper heart chambers and ventricular septal defects are openings between the two lower heart chambers. |
| Stenosis |
A narrowing of the heart's valves. This congenital defect can occur in the pulmonary (lung) or aortic (the main heart artery) valve. |
| Tetralogy of Fallot |
A cyanotic defect in which the blood pumped through the body has too little oxygen. Tetralogy of Fallot includes four defects: a large hole between the ventricles, narrowing at or beneath the pulmonary valve, an overly muscular right ventricle, and an aorta over the large hole. |
| Transposition of the great arteries |
A cyanotic defect in which the blood pumped through the body has too little oxygen. The pulmonary artery and the aorta are reversed. |
Record Number: DU2601000632
SOURCE: "Heart surgery for congenital defects." Lori De Milto, MD. The Gale Encyclopedia of Medicine. Second Edition. Jacqueline L. Longe, Editor. 5 vols. Farmington Hills, MI: Gale Group, 2001.
|